Glycogen storage disease type I and G6Pase-β deficiency: etiology and therapy JY Chou, HS Jun, BC Mansfield Nature Reviews Endocrinology 6 (12), 676-688, 2010 | 243 | 2010 |
Type I glycogen storage diseases: disorders of the glucose-6-phosphatase/glucose-6-phosphate transporter complexes JY Chou, HS Jun, BC Mansfield Journal of inherited metabolic disease 38, 511-519, 2015 | 133 | 2015 |
Impaired neutrophil activity and increased susceptibility to bacterial infection in mice lacking glucose-6-phosphatase–β YY Cheung, SY Kim, WH Yiu, CJ Pan, HS Jun, RA Ruef, EJ Lee, ... The Journal of clinical investigation 117 (3), 784-793, 2007 | 131 | 2007 |
Molecular mechanisms of neutrophil dysfunction in glycogen storage disease type Ib HS Jun, DA Weinstein, YM Lee, BC Mansfield, JY Chou Blood, The Journal of the American Society of Hematology 123 (18), 2843-2853, 2014 | 122 | 2014 |
Neutropenia in type Ib glycogen storage disease JY Chou, HS Jun, BC Mansfield Current opinion in hematology 17 (1), 36-42, 2010 | 110 | 2010 |
Lack of glucose recycling between endoplasmic reticulum and cytoplasm underlies cellular dysfunction in glucose-6-phosphatase-β–deficient neutrophils in a congenital … HS Jun, YM Lee, YY Cheung, DH McDermott, PM Murphy, SS De Ravin, ... Blood, The Journal of the American Society of Hematology 116 (15), 2783-2792, 2010 | 100 | 2010 |
Neutrophil stress and apoptosis underlie myeloid dysfunction in glycogen storage disease type Ib SY Kim, HS Jun, PA Mead, BC Mansfield, JY Chou Blood, The Journal of the American Society of Hematology 111 (12), 5704-5711, 2008 | 96 | 2008 |
Quantitative proteomic analysis of Niemann-Pick disease, type C1 cerebellum identifies protein biomarkers and provides pathological insight SM Cologna, XS Jiang, PS Backlund, CVM Cluzeau, MK Dail, ... PloS one 7 (10), e47845, 2012 | 93 | 2012 |
Severe congenital neutropenia resulting from G6PC3 deficiency with increased neutrophil CXCR4 expression and myelokathexis DH McDermott, SS De Ravin, HS Jun, Q Liu, DAL Priel, P Noel, ... Blood, The Journal of the American Society of Hematology 116 (15), 2793-2802, 2010 | 91 | 2010 |
Prevention of hepatocellular adenoma and correction of metabolic abnormalities in murine glycogen storage disease type Ia by gene therapy YM Lee, HS Jun, CJ Pan, SR Lin, LH Wilson, BC Mansfield, JY Chou Hepatology 56 (5), 1719-1729, 2012 | 82 | 2012 |
Outer Membrane Proteins of Fibrobacter succinogenes with Potential Roles in Adhesion to Cellulose and in Cellulose Digestion HS Jun, M Qi, J Gong, EE Egbosimba, CW Forsberg Journal of bacteriology 189 (19), 6806-6815, 2007 | 81 | 2007 |
SLC37A1 and SLC37A2 are phosphate-linked, glucose-6-phosphate antiporters CJ Pan, SY Chen, HS Jun, SR Lin, BC Mansfield, JY Chou PloS one 6 (9), e23157, 2011 | 77 | 2011 |
Characterization and Synergistic Interactions of Fibrobacter succinogenes Glycoside Hydrolases M Qi, HS Jun, CW Forsberg Applied and Environmental Microbiology 73 (19), 6098-6105, 2007 | 71 | 2007 |
Cel9D, an Atypical 1,4-β-d-Glucan Glucohydrolase from Fibrobacter succinogenes: Characteristics, Catalytic Residues, and Synergistic Interactions with Other … M Qi, HS Jun, CW Forsberg Journal of bacteriology 190 (6), 1976-1984, 2008 | 65 | 2008 |
Glucose-6-phosphatase-β, implicated in a congenital neutropenia syndrome, is essential for macrophage energy homeostasis and functionality HS Jun, YY Cheung, YM Lee, BC Mansfield, JY Chou Blood, The Journal of the American Society of Hematology 119 (17), 4047-4055, 2012 | 53 | 2012 |
G-CSF improves murine G6PC3-deficient neutrophil function by modulating apoptosis and energy homeostasis HS Jun, YM Lee, KD Song, BC Mansfield, JY Chou Blood, The Journal of the American Society of Hematology 117 (14), 3881-3892, 2011 | 52 | 2011 |
Sea buckthorn leaf extract inhibits glioma cell growth by reducing reactive oxygen species and promoting apoptosis SJ Kim, E Hwang, SS Yi, KD Song, HK Lee, TH Heo, SK Park, YJ Jung, ... Applied biochemistry and biotechnology 182, 1663-1674, 2017 | 40 | 2017 |
Fibrobacter succinogenes, a dominant fibrolytic ruminal bacterium: transition to the post genomic era HS Jun, M Qi, JK Ha, CW Forsberg Asian-Australasian Journal of Animal Sciences 20 (5), 802-810, 2007 | 39 | 2007 |
The SLC37 family of phosphate-linked sugar phosphate antiporters JY Chou, HS Jun, BC Mansfield Molecular aspects of medicine 34 (2-3), 601-611, 2013 | 36 | 2013 |
Glycogen storage disease type Ib: role of glucose‐6‐phosphate transporter in cell metabolism and function SW Sim, DA Weinstein, YM Lee, HS Jun FEBS letters 594 (1), 3-18, 2020 | 35 | 2020 |